A RARE CASE OF ENDOBRONCHIAL MALIGNANT PERIPHERAL NERVE SHEATH TUMOR

Abstract

Malignant schwannoma also called Malignant peripheral nerve sheath tumor (MPNST), is a rare and aggressive sarcoma that arises from the nerve sheath, with an incidence of 0.001%. It usually arises from peripheral nerves or somatic soft tissues. We describe a rare case of endobronchial Malignant peripheral nerve sheath tumor in a middle aged female who presented with right middle and lower lobe collapse. The diagnosis was made from the history, clinical examination, radiological investigations and bronchoscopy. The patient was subjected to pneumonectomy and tracheoplasty.